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KMID : 0388220080150020153
Journal of the Korean Rheumatism Association
2008 Volume.15 No. 2 p.153 ~ p.158
Wegener¡¯s Granulomatosis Presenting as Pyoderma Gangrenosum
Nam Seung-Joo

Ji Jong-Dae
Song Gwan-Gyu
Lee Young-Ho
Woo Jin-Hyun
Choi Seong-Jae
Abstract
Wegener¡¯s granulomatosis is multi-systemic disease characterized by granulomatous necrotizing vasculitis and it usually affects upper and lower respiratory tracts. Cutaneous manifestation as an initial presentation is unusual and comprises about 15% of cases. The most frequent skin lesions are palpable purpura, papules, ulcerations, vesicles, subcutaneous nodules, necrotizing ulcerations. We report a patient with Wegener¡¯s granulomatosis who presents as a pyoderma gangrenosum.
KEYWORD
Wegener granulomatosis, Pyoderma gangrenosum, Skin Manifestations
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